Results for fumaryloacetooctanu translation from Polish to Swedish

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Polish

fumaryloacetooctanu

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Polish

10 tyrozyny u pacjentów z ht- 1, nityzynon przeciwdziała kumulacji toksycznych półproduktów - maleiloacetooctanu i fumaryloacetooctanu.

Swedish

genom hämning av tyrosinets normala katabolism hos patienter med ht- 1, förhindrar nitisinon ansamling av de toxiska intermediaten maleylacetoacetat och fumarylacetoacetat.

Last Update: 2012-04-11
Usage Frequency: 6
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Polish

zaburzenie biochemiczne w dziedzicznej tyrozynemii typu 1 (ht- 1) polega na braku hydrolazy fumaryloacetooctanu - końcowego enzymu na szlaku katabolicznym tyrozyny.

Swedish

den biokemiska defekten vid hereditär tyrosinemi typ 1 (ht- 1) är brist på fumarylacetoacetathydrolas som är det slutliga enzymet i tyrosinets katabolism.

Last Update: 2012-04-11
Usage Frequency: 2
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