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sygdomme i forbindelse med oplagring af mucopolysakkarid skyldes mangel på de specifikke lysosomal- enzymer, der er nødvendige for glykosaminoglycanernes (gag) katabolisme.
mucopolysaccharide storage disorders are caused by the deficiency of specific lysosomal enzymes required for the catabolism of glycosaminoglycans (gags).
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