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iduronate 2-sulfatase
factor correctivo de hunter
Last Update: 2014-12-09
Usage Frequency: 1
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iduronate-2-sulfatase
iduronate-2-sulfatase
Last Update: 2011-10-23
Usage Frequency: 1
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déficite en iduronate 2-sulfatase
mucopolisacaridosis ii
Last Update: 2014-12-09
Usage Frequency: 3
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l-iduronate 2-sulfate 2-sulfohydrolase
factor correctivo de hunter
Last Update: 2014-12-09
Usage Frequency: 1
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le syndrome de hunter est une affection liée au chromosome x due à un déficit en iduronate-2- sulfatase (enzyme lysosomale).
el síndrome de hunter es una enfermedad vinculada al cromosoma x, causada por niveles insuficientes de la enzima lisosomal iduronato-2-sulfatasa.
Last Update: 2017-04-26
Usage Frequency: 2
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la substance active d’elaprase est l’idursulfase, une forme de l’enzyme humaine iduronate-2- sulfatase.
el principio activo es la idursulfasa, que es una forma de la enzima humana iduronato-2-sulfatasa.
Last Update: 2017-04-26
Usage Frequency: 2
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le principe actif d’elaprase, l’idursulfase, est une copie de l’enzyme humaine iduronate-2-sulfatase.
el principio activo de elaprase, la idursulfasa, es una copia de la enzima humana iduronato-2-sulfatasa.
Last Update: 2017-04-26
Usage Frequency: 1
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l’iduronate-2-sulfatase joue un rôle dans le catabolisme du dermatane sulfate et de l’héparane sulfate (glycosaminoglycanes – gag) en clivant les portions sulfate liées à l’oligosaccharide.
la iduronato-2-sulfatasa funciona para catabolizar los glicosaminoglicanos (gag) dermatan sulfato y heparan sulfato por escisión de los grupos sulfatos ligados a los oligosacáridos.
Last Update: 2017-04-26
Usage Frequency: 3
Quality: