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Το εν λογω ένζυμο μετέχει στο πρώτο στάδιο παραγωγής γλυκοσφιγγολιπιδίων.
this enzyme is involved in the first step of the production of glycosphingolipids.
Última atualização: 2017-04-26
Frequência de uso: 3
Qualidade:
Αναστέλλοντας τη λειτουργία του ενζύμου, η μιγλουστάτη μειώνει την παραγωγή των γλυκοσφιγγολιπιδίων στα κύτταρα.
by preventing the enzyme from working, miglustat can reduce the production of glycosphingolipids in cells.
Última atualização: 2012-04-11
Frequência de uso: 2
Qualidade:
Οι νευρολογικές εκδηλώσεις θεωρούνται δευτερεύουσες της μη- φυσιολογικής συσσώρευσης γλυκοσφιγγολιπιδίων στούς νευρώνες και στα νευρογλοιακά κύτταρα.
the neurological manifestations are considered secondary to the abnormal accumulation of glycosphingolipids in neuronal and glial cells.
Última atualização: 2017-04-26
Frequência de uso: 2
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Το zavesca δρα αναστέλλοντας το ένζυμο ‘συνθετάση του γλυκοσυλιοκεραμιδίου’ που είναι υπεύθυνο για το πρώτο στάδιο της σύνθεσης των περισσότερων γλυκοσφιγγολιπιδίων.
zavesca works by inhibiting the enzyme called ‘glucosylceramide synthase’ which is responsible for the first step in the synthesis of most glycosphingolipids.
Última atualização: 2017-04-26
Frequência de uso: 3
Qualidade:
Εάν έχετε νόσο niemann-pick τύπου c, λιπίδια όπως τα γλυκοσφιγγολιπίδια συσσωρεύονται στα κύτταρα του εγκεφάλου σας.
if you have niemann-pick type c disease, fats such as glycosphingolipids build up in the cells of your brain.
Última atualização: 2017-04-26
Frequência de uso: 3
Qualidade: