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mucopolysaccharider, glycosaminoglycaner, chondroitinsulfat- og dermatansulfatholdige, hud-
mucopolysaccharides, glycosaminoglycans, chondroitin sulfate-dermatan sulfate-contg., skin
最后更新: 2014-11-07
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normalt nedbryder dette enzym en type kulhydrater, der kaldes glycosaminoglycaner (gag) .
this enzyme normally breaks down carbohydrates known as glycosaminoglycans (gags) .
最后更新: 2008-03-04
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denne sygdom forårsages af mangel på et enzym kaldet arylsulfatase b, som er nødvendigt for at nedbryde stoffer i kroppen kaldet glycosaminoglycaner (gag).
this disease is caused by the lack of an enzyme called arylsulfatase b, which is needed to break down substances in the body called glycosaminoglycans (gags).
最后更新: 2012-04-12
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mucopolysaccharidose skyldes mangel på specifikke lysosomale enzymer, der er nødvendige i kataboliseringen af glycosaminoglycans (gags).
mucopolysaccharide storage disorders are caused by the deficiency of specific lysosomal enzymes required for the catabolism of glycosaminoglycans (gags).
最后更新: 2017-04-26
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