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pheburane sa indikuje ako prídavná liečba pri chronickom manažmente porúch močovinového cyklu vrátane deficitu karbamylfosfátsyntetázy, ornitíntranskarbamylázy alebo arginínosukcinátsyntetázy.
pheburane is indicated as adjunctive therapy in the chronic management of urea cycle disorders, involving deficiencies of carbamylphosphate synthetase, ornithine transcarbamylase or argininosuccinate synthetase.
Last Update: 2017-04-26
Usage Frequency: 1
Quality:
ammonaps sa indikuje ako prídavná liečba pri chronickom manažmente porúch močovinového cyklu, vrátane deficitu karbamylfosfátsyntetázy, ornitíntranskarbamylázy alebo arginínosukcinátsyntetázy.
ammonaps is indicated as adjunctive therapy in the chronic management of urea cycle disorders, involving deficiencies of carbamylphosphate synthetase, ornithine transcarbamylase or argininosuccinate synthetase.
Last Update: 2017-04-26
Usage Frequency: 2
Quality:
suplementácia arginínu sa vyžaduje u pacientov s diagnostikovaným deficitom arginínosukcinátsyntetázy v dávke 0,4 - 0,7 g/kg/deň alebo 8,8 – 15,4 g/m2/deň.
arginine supplementation is required for patients diagnosed with deficiency of argininosuccinate synthetase at a dose of 0.4 - 0.7 g/kg/day or 8.8 - 15.4 g/m2/day.
Last Update: 2017-04-26
Usage Frequency: 5
Quality: