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miglustaat pärsib glükosüültseramiidi süntaasi, mis vastutab esimese sammu eest enamiku glükolipiidide sünteesis.
miglustat is an inhibitor of glucosylceramide synthase, the enzyme responsible for the first step in the synthesis of most glycolipids.
Last Update: 2017-04-26
Usage Frequency: 3
Quality:
imiglütseraas (rekombinantne makrofaagide märklaud β- glükotserebrosidaas) katalüüsib glükolipiidide, glükotserebrosiidi hüdrolüüsi glükoosiks ja tseramiidiks, järgides membraani lipiidide normaalse lõhustumise ahelat.
imiglucerase (recombinant macrophage targeted β -glucocerebrosidase) catalyses the hydrolysis of the glycolipid, glucocerebroside, to glucose and ceramide following the normal degradation pathway for membrane lipids.
Last Update: 2012-04-11
Usage Frequency: 2
Quality: