전문 번역가, 번역 회사, 웹 페이지 및 자유롭게 사용할 수 있는 번역 저장소 등을 활용합니다.
choroba gauchera jest zaburzeniem genetycznym powodowanym brakiem lub uszkodzeniem enzymu o nazwie glukocerebrozydaza.
gaucher disease is a genetic disorder caused by a missing or defective enzyme named glucocerebrosidase.
마지막 업데이트: 2017-04-26
사용 빈도: 1
품질:
osoby z chorobą gaucher’ a mają niską aktywność enzymu o nazwie β- glukocerebrozydaza.
people with gaucher disease have low levels of an enzyme called β -glucocerebrosidase.
마지막 업데이트: 2012-04-12
사용 빈도: 2
품질:
enzymy – imigluceraza (rekombinowana β- glukocerebrozydaza ukierunkowana na makrofagi), kod atc:
enzymes-imiglucerase (recombinant macrophage targeted β - glucocerebrosidase), atc code:
마지막 업데이트: 2012-04-12
사용 빈도: 2
품질:
monomer ma masę około 63 kda, posiada 497 aminokwasów i taką samą sekwencję aminokwasów co występujący naturalnie ludzki enzym - glukocerebrozydaza.
the monomer is approximately 63 kda, has 497 amino acids, and the same amino acid sequence as the naturally occurring human enzyme, glucocerebrosidase.
마지막 업데이트: 2017-04-26
사용 빈도: 1
품질:
grupa farmakoterapeutyczna: enzymy – imigluceraza (rekombinowana β- glukocerebrozydaza ukierunkowana na makrofagi), kod atc:
enzymes-imiglucerase (recombinant macrophage targeted β - glucocerebrosidase), atc code:
마지막 업데이트: 2012-04-12
사용 빈도: 2
품질:
grupa farmakoterapeutyczna: enzymy – imigluceraza (rekombinowana -glukocerebrozydaza ukierunkowana na makrofagi), kod atc: a16ab02.
pharmacotherapeutic group: enzymes-imiglucerase (recombinant macrophage targeted - glucocerebrosidase), atc code: a16ab02.
마지막 업데이트: 2017-04-26
사용 빈도: 1
품질:
imigluceraza (rekombinowana β- glukocerebrozydaza ukierunkowana na makrofagi) katalizuje reakcję hydrolizy glikolipidu i, glukocerebrozydu do glukozy i ceramidu zgodnie z naturalną drogą degradacji lipidów błony komórkowej.
imiglucerase (recombinant macrophage targeted β -glucocerebrosidase) catalyses the hydrolysis of the glycolipid, glucocerebroside, to glucose and ceramide following the normal degradation pathway for membrane lipids.
마지막 업데이트: 2012-04-12
사용 빈도: 2
품질: