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choroba gauchera jest zaburzeniem genetycznym powodowanym brakiem lub uszkodzeniem enzymu o nazwie glukocerebrozydaza.
gaucher disease is a genetic disorder caused by a missing or defective enzyme named glucocerebrosidase.
Son Güncelleme: 2017-04-26
Kullanım Sıklığı: 1
Kalite:
osoby z chorobą gaucher’ a mają niską aktywność enzymu o nazwie β- glukocerebrozydaza.
people with gaucher disease have low levels of an enzyme called β -glucocerebrosidase.
Son Güncelleme: 2012-04-12
Kullanım Sıklığı: 2
Kalite:
enzymy – imigluceraza (rekombinowana β- glukocerebrozydaza ukierunkowana na makrofagi), kod atc:
enzymes-imiglucerase (recombinant macrophage targeted β - glucocerebrosidase), atc code:
Son Güncelleme: 2012-04-12
Kullanım Sıklığı: 2
Kalite:
monomer ma masę około 63 kda, posiada 497 aminokwasów i taką samą sekwencję aminokwasów co występujący naturalnie ludzki enzym - glukocerebrozydaza.
the monomer is approximately 63 kda, has 497 amino acids, and the same amino acid sequence as the naturally occurring human enzyme, glucocerebrosidase.
Son Güncelleme: 2017-04-26
Kullanım Sıklığı: 1
Kalite:
grupa farmakoterapeutyczna: enzymy – imigluceraza (rekombinowana β- glukocerebrozydaza ukierunkowana na makrofagi), kod atc:
enzymes-imiglucerase (recombinant macrophage targeted β - glucocerebrosidase), atc code:
Son Güncelleme: 2012-04-12
Kullanım Sıklığı: 2
Kalite:
grupa farmakoterapeutyczna: enzymy – imigluceraza (rekombinowana -glukocerebrozydaza ukierunkowana na makrofagi), kod atc: a16ab02.
pharmacotherapeutic group: enzymes-imiglucerase (recombinant macrophage targeted - glucocerebrosidase), atc code: a16ab02.
Son Güncelleme: 2017-04-26
Kullanım Sıklığı: 1
Kalite:
imigluceraza (rekombinowana β- glukocerebrozydaza ukierunkowana na makrofagi) katalizuje reakcję hydrolizy glikolipidu i, glukocerebrozydu do glukozy i ceramidu zgodnie z naturalną drogą degradacji lipidów błony komórkowej.
imiglucerase (recombinant macrophage targeted β -glucocerebrosidase) catalyses the hydrolysis of the glycolipid, glucocerebroside, to glucose and ceramide following the normal degradation pathway for membrane lipids.
Son Güncelleme: 2012-04-12
Kullanım Sıklığı: 2
Kalite: