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alpha-galactosidase
alfa-galaktozidaza
Laatste Update: 2014-11-21
Gebruiksfrequentie: 2
Kwaliteit:
alpha-galactosidase:
alfa-galaktozidaze:
Laatste Update: 2014-11-21
Gebruiksfrequentie: 1
Kwaliteit:
50 u alpha-galactosidase
50 u alfa-galaktozidaze
Laatste Update: 2014-11-21
Gebruiksfrequentie: 1
Kwaliteit:
fabrazyme is designed to replace the human enzyme alpha galactosidase a, which is lacking in patients with fabry disease.
zdravilo fabrazyme je zasnovano tako, da nadomesti človeški encim alfa galaktozidaza a, ki ga primanjkuje pri ljudeh s fabryjevo boleznijo.
fabrazyme is designed to replace the human enzyme alpha-galactosidase a, which people with fabry disease are lacking.
zdravilo fabrazyme je namenjeno nadomeščanju človeškega encima α- galaktozidaze a, ki ga primanjkuje pri ljudeh s fabryjevo boleznijo.
replagal is designed to replace the human enzyme alpha-galactosidase a, which is lacking in people with fabry disease.
zdravilo replagal je namenjeno nadomeščanju človeškega encima alfa-galaktozidaze a, ki ga primanjkuje osebam s fabryjevo boleznijo.
the active substance in galafold, migalastat, attaches to certain unstable forms of alpha-galactosidase a, stabilising the enzyme.
zdravilna učinkovina zdravila galafold, migalastat, se veže na določene nestabilne oblike α- galaktozidaze a in s tem stabilizira encim.
colorimetric method measuring p-nitrophenol released by action of alpha-galactosidase from p-nitrophenyl-alpha-galactopyranoside substrate,
kolorimetrična metoda merjenja p-nitrofenola, ki se med delovanjem alfa-galaktozidaze sprosti iz substrata p-nitrofenil-alfa-galaktopiranozida,
patients with fabry disease do not have enough of an enzyme called alpha-galactosidase a. this enzyme normally breaks down a fatty substance called globotriaosylceramide (gb3 or gl-3).
bolniki s fabryjevo boleznijo nimajo dovolj encima, imenovanega alfa-galaktozidaza a. ta encim običajno razgrajuje maščobno snov, imenovano globotriaozilceramid (gb3 ali gl-3 ).